Facebook post by University of Helsinki

In humans, mitochondrial DNA encodes only 13 proteins essential for energy metabolism. Defects in the faithful synthesis of these proteins represents the largest group of inherited human mitochondrial disorders. Researchers have now solved a molecular puzzle associated with genetic mutations linked to a multifaceted neurological syndrome.
Preventing the production of toxic mitochondrial proteins helsinki.fi

Researchers uncovered the mechanisms for a novel cellular stress response arising from the toxicity of newly synthesized proteins.